J Thorac Imaging 1998 Jan;13(1):49-51
Pulmonary capillary hemangiomatosis: radiographic appearance.
Lippert JL, White CS, Cameron EW, Sun CC, Liang X, Rubin LJ
Pulmonary capillary hemangiomatosis is a rare disorder that is characterized
pathologically by formation of capillaries along alveolar walls that may
ultimately invade the pulmonary parenchyma and pulmonary arteries. The
clinic presentation overlaps that of primary pulmonary hypertension, but
the natural history of pulmonary capillary hemangiomatosis is one of rapid
deterioration. The typical radiographic appearance is a diffuse bilateral
reticulonodular pattern associated with enlarged central pulmonary arteries.
