Cardiac > Adultdz > ARVD

Revised Criteria for the Diagnosis of ARVD (Radiographics 2014; Rastegar N, et al. Cardiac MR findings and potential diagnostic pitfalls in patients evaluated for arrhythmogenic right ventricular cardiomyopathy. 34: 1553-1570):

Major Criteria:

Two-dimensional echo:
1- Regional RV akinesia, dyskinesia, or aneurysm; PLUS one of the following-
- Parasternal long axis RVOT ≥ 32 mm or parasternal short axis RVOT ≥ 36 mm
- Fractional area change ≤ 33%
MR imaging:
1- Regional RV akinesia, dyskinesia, or dyssynchrony; PLUS one of the following-
- Ratio of RV- end diastolic volume to body surface area ≥ 110 mL/m2 (male) or ≥ 100 mL/m2 (female)
- RVEF ≤ 40%
Minor Criteria:

Two-dimensional echo:
1- Regional RV akinesia, dyskinesia, or aneurysm; PLUS one of the following-
- Parasternal long axis RVOT ≥ 29 < 32 mm or parasternal short axis RVOT ≥ 32 < 36 mm
- Fractional area change of 33-40%
MR imaging::
1- Regional RV akinesia, dyskinesia, or dyssynchrony; PLUS one of the following-
- Ratio of RV- end diastolic volume to body surface area ≥ 100 to < 110 mL/m2 (male) or ≥ 90 to < 100 mL/m2 (female)
- RVEF > 40% to ≤ 45%
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