Chest radiograph on a six-year-old girl.
Findings: The plain radiographs demonstrate a left apical mass with splaying of the ribs and abnormal spinal contour. The CT demonstrates a paravertebral soft tissue mass in the left apex. There is dural ectasia, expansion of the neuroforamina, and and scalloping of the vertebral bodies. The MR demonstrates multiple enhancing heterogenous T2 hyper intense masses in the left paravertebral region centered in the upper thoracic spine with dural ectasia and lateral thoracic meningoceles.
- Plexiform neurofibroma
- Chronic inflammatory demyelinating polyneuropathy
Diagnosis: Plexiform neurofibroma
Which choice best depicts the syndrome associated with this diagnosis?Von Recklinghausen disease.Neurofibromatosis type 1.Neurofibromatosis type 2.A or B.A or C.